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http://worldcat.org/entity/work/id/69683898

The ragin' Cajun Usher syndrome

Neurologist Oliver Sacks takes a look at Usher's syndrome, a condition which includes congenital deafness and advancing blindness through adolescence and middle age. Usher's syndrome has its highest concentration in the Cajun population. A large group of Cajuns with Usher's syndrome have moved to Seattle, Washington. Danny Delcambre leads Oliver Sacks into their world.

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http://schema.org/about

http://schema.org/alternateName

  • "Ragun cajun"
  • "Monochromatism"
  • "Usher syndrome"@en
  • "Usher syndrome"

http://schema.org/description

  • "Neurologist Oliver Sacks takes a look at Usher's syndrome, a condition which includes congenital deafness and advancing blindness through adolescence and middle age. Usher's syndrome has its highest concentration in the Cajun population. A large group of Cajuns with Usher's syndrome have moved to Seattle, Washington. Danny Delcambre leads Oliver Sacks into their world."@en
  • "This program takes a look at Usher syndrome; as neurologist/author Oliver Sacks and Danny Delcambre explore the nature of deaf culture and American Sign Language."@en
  • "This program takes a look at the degenerative hearing condition, Usher syndrome. Neurologist/author Oliver Sacks and Danny Delcambre explore the nature of deaf culture and the richness of American Sign Language, which includes a sophisticated touch-based variation called tactile signing."@en
  • "Explores deaf culture and American Sign Language by following the life of Danny Delcambre, who has Usher syndrome. Born in a region of Louisiana which has the highest concentration of Usher syndrome in the world, Danny, who was deaf from birth and losing his sight, moved to a thriving deaf-blind community in Seattle."
  • "Fifth episode in a 6-part series in which Dr. Oliver Sacks travels the world in search of cases of rare neurological disorders and compares his findings with existing knowledge of these diseases. The title leads one to expect an encounter with a severely disturbed person but it turns out to be the name of a restaurant run by Danny Delcombe who has Usher's syndrome. This is a genetic condition whereby a child is born deaf and suffers deteriorating vision in adolescence which diminishes to tunnel vision and eventual blindness. Usher's syndrome originated in Nova Scotia, Canada, from which thousands of French farmers were expelled by the British in the 18th century, many of whom settled around Louisiana in what came to be known as Cajun country (from Arcadia, the old name for Nova Scotia). In this tight community inter-marriage and incest multiplied the defective gene and this region now has the world's highest concentration of people with Usher's syndrome. Unable to find employment in Louisiana, Danny moved to Seattle, a city which is very aware of the problems of the deaf-blind. He found a strong community of Usher's syndrome people there and eventually opened his own restaurant which is staffed by people with this condition. It quickly became an important aspect of their community life. Oliver Sacks became involved in the life of this community; he explores the history and structure of American Sign Language and its adapted tactile form used by those both deaf and blind. This is further analysed by Dr. Ursula Belugi (neurolinguist). The film is an impressive record of optimism and achievement in the face of severe disability."@en

http://schema.org/genre

  • "Interviews"@en
  • "Documentary television programs"@en
  • "Documentary television programs"
  • "Videocassettes"@en

http://schema.org/name

  • "The ragin' Cajun Usher syndrome"@en
  • "The ragin' Cajun Usher syndrome"
  • "The Ragin' Cajun usher syndrome"@en
  • "Ragin' Cajun"
  • "Ragin' cajun"
  • "The ragin' Cajun"@en
  • "The ragin' cajun"
  • "The Ragin Cajun"@en
  • "The Ragin Cajun"